Cystic Fibrosis Center
Cystic fibrosis (CF) is an inherited chronic disease that affects the lungs and digestive system of about 40,000 children and adults in the United States. Cystic fibrosis (CF) is a complex, life-threatening, inherited disease that can cause respiratory, digestive, and reproductive problems, and malnutrition. Early detection and treatment of CF is key to increasing life expectancy, slowing the progression of the disease and preventing complications.
Blank Children's Hospital is fully accredited by the Cystic Fibrosis Foundation to care for patients with CF. The CF center brings together an integrated team of pulmonology, gastroenterology, endocrinology, dietary, pharmacy, social work, physical therapy and Child Life for a convenient appointment for patients and families. We are one of two hospitals in the state offering this type of clinic. We see patients of all ages - pediatric through adult.
Appointments with our team include a visit with:
- A Pulmonologist/Nurse Practitioner
- Registered Dietitian
- Respiratory Therapist
- Physical Therapist
- Social Worker
- Child Life Specialist
- Genetics Counselor
What to Expect at Your First Visit
Your first visit to Blank Cystic Fibrosis Center will probably be the longest. Please plan to be at the clinic for approximately two to four hours. We ask that you arrive 15 to 20 minutes ahead of your appointment to complete medical history and insurance information forms.
Please bring the following items to each appointment:
- Photo ID
- Current Insurance Card
- List of Current Medications
Frequently Asked Questions
What is a sweat test?
The sweat test is a definitive test to diagnose CF.
What to expect with a sweat test?
A sweat test uses is a small, non-painful, electric current to carry the chemical pilocarpine into the skin of the forearm. This stimulates sweat glands in the area to produce sweat. The sweat is collected in and placed in a small tube and the chloride (salt) content is tested.
Do I need genetic testing?
The state of Iowa tests all newborns for CF at birth. Most infants who screen positive do not have CF but are likely carriers of CF. When genetic testing is performed, patients will meet with a genetic counselor and providers the same-day to discuss results.
Do I still need a primary care doctor?
Yes, you will still need to see your primary care doctor to handle your routine care. Your CF team will collaborate with your primary doctor if needed.
If you do not have a primary care provider, establishing care has never been easier! To schedule an appointment at a pediatric clinic near you, simply call the clinic or request an appointment online.
How often do I need to see the CF team?
Adults 3-4 times a year or more frequently depending on patient disease state. Children we follow the CF recommendations or may see more frequently depending on patient disease state
How often will I need labs and X-rays?
At least annually and more frequently depending on patient disease state